A 5-year-old tracheostomy-dependent patient presents to pediatric otolaryngology for follow-up. The patient was born at 32 weeks gestation, and has a complex medical history that includes chronic lung disease, pulmonary hypertension, respiratory failure, achondroplasia and an autism diagnosis. In this case study, pediatric otolaryngologist Brandon Hopkins, MD, discusses factors that should be considered in a decision to progress to decannulation.
Since multiple conditions can mimic components of PAH, the clinician should think about the patient’s total clinical condition before diagnosing and categorizing it. Proper evaluation and etiologic definition are crucial to providing the appropriate therapy and prognosis.
The TRAIL-1 study explores the use of pirfenidone, an antifibrotic agent approved for idiopathic pulmonary fibrosis, in patients with rheumatoid arthritis-associated interstitial lung disease.
Interest in right-sided heart failure is on the upswing, but no formal statement has considered all major topics relevant to this syndrome. A new document from the AHA changes that.
Cleveland Clinic is a non-profit academic medical center. Advertising on our site helps support our mission. We do not endorse non-Cleveland Clinic products or services Policy
While the incidence of CTEPH is low, diagnosis is important by a specialized multidisciplinary program that can provide a surgical cure.