A 3D-Printed Window Into Biventricular Repair of Adult Heterotaxy

This is a 30-year-old man who was born with heterotaxy, double-outlet right ventricle with pulmonary stenosis and a common AVSD [atrioventricular septal defect] on the inside of the heart. Has bilateral superior vena cava and a hepatic vein that opens separate from the IVC [inferior vena cava], and total anomalous pulmonary venous drainage that opens into the back of the left SVC [superior vena cava]. He presented to us with cyanosis and a previous stroke, and we were wondering whether we could offer him a biventricular repair. By doing this 3D model printing, we were able to see that the two ventricles are of good size. The left ventricle is very far from the aorta. Therefore, we decided to make that left ventricle as the supplementary ventricle. We needed to reroute his systemic venous return to the left component of the AVSD and then crate a left ventricle-to-pulmonary artery conduit. And we connected the pulmonary veins into the right atrium, which became the pulmonary venous atrium that connects to the right ventricle and to the aorta.